Goldenhar syndrome (oculo-auriculo-vertebral dysplasia) in a twin new born baby.

نویسندگان

  • M M Faridi
  • S Ahmad
  • R Moonis
  • Z Ansari
  • S K Bhargava
چکیده

Fhe Oculo-auriculo-vertebral dyspla~ia, described for the first time by Goldenhar 1 is a disorder affecting the structures which develop from I and II branchial archs. It is characterised by epibulbar dermoid cyst and preauricular skin appendages with or without vertebral defects. 2 This syndrome has always been reported in single born babies from India 2-4 but in western literature 3 cases have been described in one of the twins. 5 We have also studied a case of Goldenhar syndrome in one of the male twins delivered at JN Medical College Hospital, AMU, Aligarh. The other male twin baby was apparantly normal which is quite interesting and is the first case of its kind from India.

برای دانلود رایگان متن کامل این مقاله و بیش از 32 میلیون مقاله دیگر ابتدا ثبت نام کنید

ثبت نام

اگر عضو سایت هستید لطفا وارد حساب کاربری خود شوید

منابع مشابه

Audiological Findings in Patients with Oculo-Auriculo-Vertebral Spectrum

Introduction Oculo-auriculo-vertebral spectrum, also referred to as Goldenhar syndrome, is a condition characterized by alterations involving the development of the structures of the first and second branchial arches. The abnormalities primarily affect the face, the eyes, the spine, and the ears, and the auricular abnormalities are associated with possible hearing loss. Objective To analyze the...

متن کامل

Goldenhar Syndrome and Pericentric Inversion of Chromosome 9

Oculo-auriculovertebral dysplasia (Goldenhar) is a congenital syndrome. Its phenotype differs from craniofacial anomalies to cardiac, vertebral or central nervous system defects. This syndrome is rare and its etiology is not apparent yet. Pericentric inversion of chromosome 9 is one of the most common structural balanced chromosomal aberrations with its incidences 15% to 25%. Herein we present ...

متن کامل

Cranial Nerve Abnormalities in Oculo-Auriculo-Vertebral Spectrum.

BACKGROUND AND PURPOSE Cranial nerve abnormalities might be observed in hemifacial microsomia and microtia (oculo-auriculo-vertebral spectrum), but the rate, features, and relationship with functional impairment or phenotype severity have not yet been defined. This study aimed at investigating absence/asymmetry, abnormal origin, morphology and course of cranial nerves, and presence/asymmetry of...

متن کامل

Craniofacial abnormalities in goldenhar syndrome: a case report with review of the literature

Goldenhar syndrome (oculo-auriculo-vertebral spectrum) is a rare congenital anomaly of unclear etiology and characterized by craniofacial anomalies such as hemifacial microsomia, auricular, ocular and vertebral anomalies. In many cases, this syndrome goes unnoticed due to a lack of knowledge about its features and because of its associated wide range of overlapping anomalies. Herewith, we prese...

متن کامل

Goldenhar's syndrome--case report.

Goldenhar's syndrome is a rare condition described initially in the early 1950's. It is characterized by a combination of anomalies: dermal epibulbar cysts, auricular appendices and malformation of the ears. In 1963, Gorlin suggested the name oculo-auriculo-vertebral (OAV) dysplasia for this condition and also included vertebral anomalies as signs of the syndrome. The etiology of this rare dise...

متن کامل

ذخیره در منابع من


  با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید

عنوان ژورنال:
  • Indian journal of pediatrics

دوره 53 2  شماره 

صفحات  -

تاریخ انتشار 1986